Guidelines for diagnosing & treating biliary atresia (2018 Edition)
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摘要:
<正>胆道闭锁(biliary atresia,BA)是婴儿期常见的严重肝胆系统疾病之一,以肝内、外胆管进行性炎症和纤维化为特征;如不及时治疗,晚期会出现胆汁性肝硬化、门静脉高压、肝衰竭。目前早期诊断困难,手术治疗效果欠佳,可能与诊断方法、Kasai手术标准化程度及该病知识普及程度有关。制订一个明确、可靠并在临床上切实可行的指南是当下亟需解决的问题。本指南涵盖近年来相关研究,将所有证据基于GRADE系
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Key words:
- biliary atresia /
- child /
- practice guidelines as topic
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[1] ATKINS D,BEST D,BRISS PA,et al. Grading quality of evidence and strength of recommendations[J]. BMJ,2004,328(7454):1490. [2] KASAI M,OKAMOTO A,OHI R,et al. Changes of portal vein pressure and intrahepatic blood vessels after surgery for biliary atresia[J]. J Pediatr Surg,1981,16(2):152-159. [3] YOON PW,BRESEE JS,OLNEY RS,et al. Epidemiology of biliary atresia:A population-based study[J]. Pediatrics,1997,99(3):376-382. [4] GIRARD M,JANNOT AS,BESNARD M,et al. Polynesian ecology determines seasonality of biliary atresia[J]. Hepatology,2011,54(5):1893-1894. [5] MCKIERNAN PJ,BAKER AJ,KELLY DA. The frequency and outcome of biliary atresia in the UK and Ireland[J]. Lancet,2000,355(9197):25-29. [6] WILDHABER BE,MAJNO P,MAYR J,et al. Biliary atresia:Swiss national study,1994-2004[J]. JPGN,2008,46(3):299-307. [7] CATON AR,DRUSCHEL CM,MCNUTT LA. The epidemiology of extrahepatic biliary atresia in New York State,1983-98[J].Paediatr Perinat Epidemiol,2004,18(2):97-105. [8] NIO M,OHI R,MIYANO T,et al. Five-and 10-year survival rates after surgery for biliary atresia:A report from the Japanese Biliary Atresia Registry[J]. J Pediatr Surg,2003,38(7):997-1000. [9] CHIU CY,CHEN PH,CHAN CF,et al. Biliary atresia in preterm infants in Taiwan:A nationwide survey[J]. J Pediatr,2013,163(1):100-103. [10] KASAI M,SAWAGUCHI M,AKIYAMA T,et al. A proposal of new classification of biliary atresia[J]. JJSPS,1976,12:327-331. [11] DAVENPORT M. Biliary atresia:Clinical aspects[J]. Semin Pediatr Surg,2012,21(3):175-184. [12] SUPERINA R,MAQEE JC,BRANDT ML,et al. The anatomic pattern of biliary atresia identified at time of Kasai hepatoportoenterostomy and early postoperative clearance of jaundice are significant predictors of transplant-free survival[J]. Ann Surg,2011,254(4):577-585. [13] DAVENPORT M,TIZZARD SA,UNDERHILL J,et al. The biliary atresia splenic malformation syndrome:A 28-year single center retrospective study[J]. J Pediatr,2006,149(3):393-400. [14] DAVENPORT M,de VILLE DE GOYET J,STRINGER MD,et al. Seamless management of biliary atresia in England and Wales(1999—2002)[J],Lancet,2004,363(9418):1354-1357. [15] LIEN TH,CHANG MH,WU JF,et al. Effects of the infant stool color card screening program on 5-year outcome of bihary atresia in Taiwan[J]. Hepatology,2011,53(1):202-208. [16] LEE M,CHEN SC,YANG HY,et al. Infant stool color card screening helps reduce the hospitalization rate and mortality of biliary atresia:A 14-year nationwide cohort study in Taiwan[J]. Medicine,2016,95(12):1-16. [17] HUMPHREY T,STRINGER M. Biliary atresia:US diagnosis[J]. Radiology,2007,244(3):845-851. [18] ZHAO W,WANG XY. The clinical application of percutaneous bilirubin tester in neonatal hyperbilirubinernia[J]. Chin J Birth Health Heredity,2003,11(4):89.(in Chinese)赵炜,王秀英.经皮胆红素测定仪在新生儿高胆红素血症中的临床应用[J].中国优生与遗传杂志,2003,11(4):89. [19] PERLMUTTER DH,SHEPHERD RW. Extrahepatic biliary atresia:A disease or a phenotype?[J]. Hepatology,2002,35(6):1297-1304. [20] WEI YY,CHEN Y,GAO T,et al. The diagnostic value of GGT combined with ultrasound found gallbladder abnormality in infants with biliary atresia[J]. Chin J Gen Surg,2017,32(5):425-428.(in Chinese)卫园园,陈扬,高婷,等.谷氨酰转肽酶测定联合超声诊断先天性胆道闭锁[J].中华普通外科杂志,2017,32(5):425-428. [21] SHEN QL,CHEN YJ,WANG ZM,et al. Assessment of liver fibrosis with transient elastography in biliary atresia[J]. Chin J Pediatr Surg,2014,35(4):275-279.(in Chinese)沈秋龙,陈亚军,王增萌,等.瞬时弹性成像应用于胆道闭锁肝纤维化评估的研究[J].中华小儿外科杂志,2014,35(4):275-279. [22] LEE JY,SULLIVAN K,EI DEMELLAWY D,et al. The value of preoperative liver biopsy in the diagnosis of extrahepatic biliary atresia:A systematic review and meta-analysis[J]. J Pediatr Surg,2016,51(5):753-761. [23] ASAI A. 50 years ago in the journal of pediatrics:Diagnosis of biliary atresia:Relative accuracy of percutaneous liver biopsy,open liver biopsy,and operative cholangiography[J]. J Pediatr,2017,189:188. [24] BEZERRA JA,SPINO C,MAGEE JC,et al. Use of corticosteroids after hepatoportoenterostomy for bile drainage in infants with biliary atresia:The START randomized clinical trial[J].JAMA,2014,311(17):1750-1759. [25] DAVENPORT M,PARSONS C,TIZZARD S,et al. Steroids in biliary atresia:Single surgeon, single centre, prospective study[J]. J Hepatol,2013,59(5):1054-1058. [26] MEYERS RL,BOOK LS,O’GORMAN MA,et al. High-dose steroids,ursodeoxycholic acid,and chronic intravenous antibiotics improve bile flow after Kasai procedure in infants with biliary atresia[J]. J Pediatr Surg,2003,38(3):406-411. [27] ZHANG J,LIN T,HUANG LM,et al. The result of medium to long term follow-ups after anti-infective therapy for recurrent cholangitis after Kasai operation[J]. J Clin Ped Sur,2016,15(1):20-22.(in Chinese)张璟,林涛,黄柳明,等.胆道闭锁术后反复发作性胆管炎抗感染治疗的中长期随访[J].临床小儿外科杂志,2016,15(1):20-22. [28] NIO M. Japanese biliary atresia registry[J]. Pediatr Surg Int,2017,33(12):1319-1325. [29] SUPERINA R. Biliary atresia and liver transplantation:Results and thoughts for primary liver transplantation in select patients[J]. Pediatr Surg Int,2017,33(12):1297-1304. [30] SOBH A,BONILLA FA. Vaccination in primary immunodeficiency disorders[J]. J Allergy Clin Immunol Pract,2016,4(6):1066-1075. [31] RUBIN LG. 2013 IDSA clinical practice guideline for vaccination of the immunocompromised host[J]. Clin Infect Dis,2014,58(3):e44-e100. [32] van MOURIK ID,BEATH SV,BROOK GA,et al. Long-term nutritional and neurodevelopmental outcome of liver transplantation in infants aged less than 12 months[J]. J Pediatr Gastroenterol Nutr,2000,30(3):269-275. [33] KASAHARA M,UMESHITA K,SAKAMOTO S,et al. Liver transplantation for biliary atresia:A systematic review[J]. Pediatr Surg Int,2017,33(12):1289-1295. [34] SUNDARAM SS,MACK CL,FELDMAN AG,et al. Biliary atresia:Indications and timing of liver transplantation and optimization of pre-transplant care[J]. Liver Transpl,2017,23(1):96-109. [35] CRUZ RJ Jr,DEW MA,MYASKOVSKY L,et al. Objective radiologic assessment of body composition in patients with endstage liver disease:Going beyond the BMI[J]. Transplantation,2013,95(4):617-622. [36] SQUIRES RH. End-stage liver disease in children[J]. Curr Treat Options Gastroenterol,2001,4:409-421. [37] ARNON R,ANNUNZIATO RA,WILLIS A,et al. Liver transplantation for children with biliary atresia in the pediatric endstage liver disease era:The role of insurance status[J]. Liver Transpl,2013,19(5):543-550. [38] SUN C,GAO W,MA N,et al. Clinical analysis of ABO-incompatible pediatric liver transplantation in 16 patients[J]. Chin J Organ Transplant,2015,36(10):577-581.(in Chinese)孙超,高伟,马楠,等.小儿ABO血型不合肝移植16例的临床分析[J].中华器官移植杂志,2015,36(10):577-581. [39] VARELA-FASCINETTO G,TREACY SJ,LILLEHEI CW,et al.Long-term results in pediatric ABO-incompatible liver transplantation[J]. Transplant Proc,1999,31(12):467-468. [40] NETO JS,FEIER FH,BIRRENBACH AL,et al. Impact of Kasai portoenterostomy on liver transplantation outcomes:A retrospective cohot study of 347 children with biliary atresia[J].Liver Transpl,2015,21(7):922-927. [41] KASAHARA M,UMESHITA K,INOMATA Y,et al. Long-term outcomes of pediatric living donor liver transplantation in Japan:An analysis of more than 2200 cases listed in the registry of the Japanese Liver Transplantation Society[J]. Am J Transplant,2013,13(7):1830-1839. [42] BARSHES NR,LEE TC,BALKRISHMAN R,et al. Orthotopic liver transplantation for biliary atresia:The US experience[J].Liver Transpl,2005,11(10):1193-1200. [43] ANDERSON CD,TURMELLE YP,DARCY M,et al. Biliary strictures in pediatric liver transplant recipients—early diagnosis and treatment results in excellent graft outcomes[J]. Pediatr Transplant,2010,14(3):358-363. [44] HEFFRON TG,PILLEN T,SMALLWOOD G,et al. Incidence,impact,and treatment of portal and hepatic venous complications following pediatric liver transplantation:A single-center12 year experience[J]. Pediatr Transplant,2010,14(6):722-729. [45] NG VL,FECTEAU A,SHEPHERD R,et al. Outcomes of 5-year survivors of pediatric liver transplantation:Report on 461children from a North American multicenter registry[J]. Pediatrics,2008,122(6):e1128-e1135. [46] DANZIGER-ISAKOV L,BUCAVALAS J. Current prevention strategies against cytomegalovirus in the studies in pediatric liver transplantation(SPLIT)centers[J]. Am J Transplant,2014,14(8):1908-1911. [47] GREEN M,MICHAELS MG. Epstein-Barr virus infection and posttransplant lymphoproliferative disorder[J]. Am J Transplant,2013,13:41-54. [48] ALLEN U,GREEN M. Prevention and treatment of infectious complications after solid organ transplantation in children[J].Pediatr Clin North Am,2010,57(2):459-479.
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