Expert consensus on diagnosis and treatment of pyrrolidine alkaloids-related sinusoidal obstruction syndrome (2017, Nanjing)
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摘要:
<正>肝窦阻塞综合征(hepatic sinusoidal obstruction syndrome,HSOS),又称肝小静脉闭塞病(hepatic venoocclusive disease,HVOD),是由各种原因导致的肝血窦、肝小静脉和小叶间静脉内皮细胞水肿、坏死、脱落进而形成微血栓,引起肝内淤血、肝损伤和门静脉高压的一种肝脏血管性疾病[1-4]。2002年,De Leve等[5]基于实验和病理研究发现,建议以HSOS代替HVOD。在近年发表的文献中上述两种名称均有使用。因此,在本共识中我们认同HSOS和HVOD可以相互替换[6]。
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Key words:
- hepatic veno-occlusive disease /
- diagnosis /
- therapy /
- consensus
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