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肝静脉阻塞型布加综合征的研究进展

郭旭 吴浩

引用本文:
Citation:

肝静脉阻塞型布加综合征的研究进展

DOI: 10.12449/JCH240102
基金项目: 

国家自然科学基金 (82270649)

四川省科技厅重点研发项目 (22ZDYF0621)

四川大学华西医院临床研究孵化重点项目 (2019HXFH024)

利益冲突声明:本文不存在任何利益冲突。
作者贡献声明:郭旭负责查阅文献、撰写论文;吴浩负责拟定文章写作方向与思路、指导论文撰写、修改与定稿。
详细信息
    通信作者:

    吴浩, hxxhwh@163.com (ORCID: 0000-0001-6751-3036)

Research advances in the diagnosis and treatment of hepatic vein occlusion-type Budd-Chiari syndrome

Research funding: 

National Natural Science Foundation of China (82270649);

Sichuan Science and Technology Program (22ZDYF0621);

Clinical Research Incubation Project, West China Hospital, Sichuan University (2019HXFH024)

More Information
    Corresponding author: WU Hao, hxxhwh@163.com (ORCID: 0000-0001-6751-3036)
  • 摘要: 布加综合征作为一种罕见的肝血管疾病,根据肝脏流出道阻塞部位不同可分为肝静脉阻塞型、下腔静脉阻塞型和混合型。本文将着重于肝静脉阻塞型,对其流行病学、亚型分型、临床诊断、治疗策略等方面进行论述。

     

  • 图  1  肝静脉阻塞型BCS治疗策略

    注: TIPS,经颈静脉肝内门体分流术;DIPS,直接肝内门体分流术。

    Figure  1.  Treatment strategy for hepatic vein occlusion type BCS

    表  1  肝静脉阻塞型BCS亚型超声成像特点

    Table  1.   Ultrasound imaging characteristics of subtypes of hepatic vein occlusion type BCS

    亚型分型 超声特点
    肝静脉/副肝静脉膜性阻塞 肝静脉和副肝静脉开口处条带样高回声,血流受阻,膜下方肝静脉管腔扩张
    肝静脉节段性阻塞 肝静脉近心段无血流
    肝静脉广泛性阻塞 肝静脉主干成条索状回声,血流信号消失
    肝静脉阻塞伴血栓形成 阻塞的肝静脉管腔内血栓回声,无血流回声
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  • 收稿日期:  2023-10-31
  • 录用日期:  2023-11-21
  • 出版日期:  2024-01-23
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