肝脾肿大伴β脂蛋白缺乏症1例报告

郭海军

doi:10.3969/j.issn.1001-5256.2022.08.031

肝脾肿大伴β脂蛋白缺乏症1例报告

DOI: 10.3969/j.issn.1001-5256.2022.08.031

郭海军^, ,

邢台市人民医院肝病科，河北邢台 054000

伦理学声明：本例报告已获得患者知情同意。

利益冲突声明：作者声明不存在利益冲突。

详细信息

通信作者:
郭海军，18631966153@163.com

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出版历程
- 收稿日期: 2021-09-12
- 录用日期: 2022-01-04
- 出版日期: 2022-08-20

Hepatosplenomegaly with β-lipoprotein deficiency: A case report

Haijun GUO^{,
,}

Department of Liver Diseases, Xingtai People's Hospital, Xingtai, Hebei 054000, China

More Information

Corresponding author: GUO Haijun, 18631966153@163.com(ORCID: 0000-0002-4863-5297)

摘要

- 低β脂蛋白血症 /
- 无β脂蛋白血症 /
- 肝肿大 /
- 脾大
- Hypobetalipoproteinemias /
- Abetalipoproteinemia /
- Hepatomegaly /
- Splenomegaly

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图 1 肝脏MR检查结果

注：a，T₁W_I；b，T₂W_I；c，动脉期；d，静脉期。

Figure 1. MR examination results of the liver

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图 2 肝脏病理结果(HE染色，×40)

Figure 2. Pathological results of the liver (HE staining, ×40)

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图 3 外周血涂片检查(瑞氏染色，×1000)

Figure 3. Peripheral blood smear examination (Wright staining, ×1000)

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参考文献(14)

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