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肝前性非肝硬化性门静脉高压症的诊疗进展

杨佳琪 尚玉龙 韩英

引用本文:
Citation:

肝前性非肝硬化性门静脉高压症的诊疗进展

DOI: 10.3969/j.issn.1001-5256.2022.07.002
基金项目: 

国家自然科学基金 (81820108005)

利益冲突声明:所有作者均声明不存在利益冲突。
作者贡献声明:杨佳琪负责收集资料并撰写文章;尚玉龙负责文稿修订;韩英负责选题,并最终审阅定稿。
详细信息
    通信作者:

    韩英,hanying@fmmu.edu.cn

Research advances in the diagnosis and treatment of prehepatic noncirrhotic portal hypertension

Research funding: 

National Natural Science Foundation of China (81820108005)

More Information
  • 摘要: 肝前性非肝硬化性门静脉高压是一组由非肝硬化因素导致的门静脉高压性疾病,目前认为这组疾病的病因主要与JAK2突变、血液高凝状态有关。临床表现主要包括静脉曲张破裂出血、脾肿大等,患者肝功能正常或仅有轻微异常。对肝前性非肝硬化性门静脉高压疾病的诊断主要依靠其影像学特点,同时还需排除肝硬化门静脉高压。治疗方面主要采取抗凝治疗和内镜下治疗,患者预后一般较好。本文系统梳理了肝前性非肝硬化性门静脉高压的主要进展。

     

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  • 收稿日期:  2022-04-20
  • 录用日期:  2022-05-23
  • 出版日期:  2022-07-20
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