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成人Still病合并巨噬细胞活化综合征致急性肝衰竭行肝移植1例报告

马海英 刘彦 李志琴 王虎 张灵强 陈虹 樊海宁

引用本文:
Citation:

成人Still病合并巨噬细胞活化综合征致急性肝衰竭行肝移植1例报告

DOI: 10.3969/j.issn.1001-5256.2020.11.031
基金项目: 

青海省包虫病临床医学研究中心资助项目(2017-SF-L2); 

详细信息
  • 中图分类号: R575.3;R597

A case of liver transplantation for acute liver failure due to adult-onset Still's disease with macrophage activation syndrome

Research funding: 

 

  • 摘要:

    <正>1病例资料患者女性,30岁,因"体检发现肝功能异常3周,皮肤巩膜黄染2周,意识障碍1 d"由北京地坛医院转入北京清华长庚医院就诊。患者于入院3周前体检时发现ALT、AST升高,后无明显诱因出现皮肤及巩膜黄染,伴发热、尿色加深,最高体温可达40℃,至北京大学第三医院就诊,查肝功能:ALT 2933 U/L,

     

  • [1] KANG LM,ZHENG Y. Adult-onset Still’s disease misdiagnosed as liver abscess:A case report and literature review[J]. J Clin Hepatol,2018,34(2):387-388.(in Chinese)康利民,郑永.成人Still病误诊为肝脓肿1例报告并文献复习[J].临床肝胆病杂志,2018,34(2):387-388.
    [2] WANG GY,SHI XJ,JIANG C,et al. One case of liver transplantation for liver failure due to adult-onset Still’s disease[J]. J Clin Hepatol,2014,30(1):67-68.(in Chinese)王广义,石小举,蒋超,等.成人Still病致肝功能衰竭行肝移植1例报告[J].临床肝胆病杂志,2014,30(1):67-68.
    [3] FEIST E,MITROVIC S,FAUTREL B. Mechanisms,biomarkers and targets for adult-onset Still’s disease[J]. Nat Rev Rheumatol,2018,14(10):603-618.
    [4] CHENG H,PAN J,YAO TT,et al. Clinical characteristics and mechanism of systemic inflammatory response induced liver injury[J]. Int J Viorl,2019,26(5):354-357.(in Chinese)程浩,潘静,姚甜甜,等.全身炎症反应导致肝损伤的临床特点和机制研究现状[J].国际病毒学杂志,2019,26(5):354-357.
    [5] SCHULERT GS,CRON RQ. The genetics of macrophage activation syndrome[J]. Genes Immun,2020,21(3):169-181.
    [6] AGNIHOTRI A,RUFF A,GOTTERER L,et al. Adult onset Still’s disease associated with mycoplasma pneumoniae infection and hemophagocytic lymphohistiocytosis[J]. Case Rep Med,2016,2016:2071815.
    [7] GOPALARATHINAM R,ORLOWSKY E,KESAVALU R,et al.Adult onset Still’s disease:A review on diagnostic workup and treatment options[J]. Case Rep Rheumatol,2016,2016:6502373.
    [8] GRIFFIN G,SHENOI S,HUGHES GC. Hemophagocytic lymphohistiocytosis:An update on pathogenesis,diagnosis,and therapy[J]. Best Pract Res Clin Rheumatol,2020:101515.
    [9] WATANABE E,SUGAWARA H,YAMASHITA T,et al. Successful tocilizumab therapy for macrophage activation syndrome associated with adult-onset Still’s disease:A casebased review[J]. Case Rep Med,2016,2016:5656320.
    [10] KOU JT,LIU Z,ZHU JQ,et al. Research on clinical efficacy of liver transplantation for severe liver disease[J]. Ogran Transplantation,2020,11(4):482-486.(in Chinese)寇建涛,刘喆,朱继巧,等.肝移植治疗危重症肝病的临床疗效研究[J].器官移植,2020,11(4):482-486.
    [11] YE ZH,ZHAO HC,HUANG F,et al. Application of smal-forsize graft of pediatric donor liver transplantation in an adult recipient with acute liver failure:A report of one case and literature review[J]. Organ Transplantation,2018,9(3):227-231.(in Chinese)叶征辉,赵红川,黄帆,等.儿童小体积供肝肝移植治疗成人急性肝衰竭1例附文献复习[J].器官移植,2018,9(3):227-231.
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  • 出版日期:  2020-11-20
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