阵发性睡眠性血红蛋白尿症致门静脉高压症1例报告

智一晓; 庞梦圆; 陶禹; 华瑞

doi:10.3969/j.issn.1001-5256.2020.01.037

阵发性睡眠性血红蛋白尿症致门静脉高压症1例报告

DOI: 10.3969/j.issn.1001-5256.2020.01.037

吉林大学第一医院肝胆胰内科

详细信息

中图分类号: R575.2;R597
计量
- 文章访问数: 907
- HTML全文浏览量: 14
- PDF下载量: 196
- 被引次数: 0
出版历程
- 出版日期: 2020-01-20

A case of portal hypertension caused by paroxysmal nocturnal hemoglobinuria

Department of Hepatology,The First Hospital of Jilin University

摘要

摘要: <正>门静脉高压症是指肝静脉压力梯度> 10 mm Hg[1]。由于门静脉压力升高将导致腹腔脏器血管压力升高,形成侧支循环,极易发生并发症,严重影响患者预后。门静脉高压症大多由肝硬化引起,少数患者存在肝前性或肝后性因素。现报道1例由肝前性和肝后性因素共同导致的门静脉高压症。1病例资料患者男性,28岁,因"间断鼻衄,PLT减少3个月"于2018年6月10日入本院就诊。患者3个月前因反复鼻衄就诊于当
- 高血压,门静脉 /
- 血红蛋白尿,阵发性 /
- 诊断
- hypertension,portal /
- hemoglobinuria,paroxysmal /
- diagnosis

HTML全文

参考文献(11)

[1] QI X,WU F,HE C,et al. Thrombotic risk factors in Chinese nonmalignant and noncirrhotic patients with portal vein thrombosis:An observational study with a systematic review of the literature[J]. Eur J Gastroenterol Hepatol,2015,27(1):77-83.

[2] WU KM,CAO S,ZHANG GY,et al. A case of paroxysmal nocturnal hemoglobinuria with Budd-Chiari syndrome as the first manifestation[J]. J Clin Hepatol,2018,34(10):2197-2199.(in Chinese)巫凯敏，曹珊，张国艳，等．以布加综合征为首发表现的阵发性睡眠性血红蛋白尿症1例报告[J]．临床肝胆病杂志，2018,34(10):2197-2199.

[3] YANG LY. Attention to the surgical treatment of portal hypertension in China[J]. Chin J Dig Surg,2018,17(10):971-975.(in Chinese)杨连粤．重视我国门静脉高压症外科治疗的问题[J]．中华消化外科杂志，2018,17(10):971-975.

[4] BOSCH J,IWAKIRI Y. The portal hypertension syndrome:Etiology,classification,relevance,and animal models[J]. Hepatol Int,2018,12(Suppl 1):1-10.

[5] HE GS. Research progress of thrombosis paroxysmal nocturnal hemoglobinuria[J]. Chin J Pract Intern Med,2014,34(8):774-776.(in Chinese)何广胜．阵发性睡眠性血红蛋白尿症的血栓形成研究进展[J]．中国实用内科杂志，2014,34(8):774-776.

[6] HILL A,KELLY RJ,HILLMEN P. Thrombosis in paroxysmal nocturnal hemoglobinuria[J]. Blood,2013,121(25):4985-4996,quiz 5105.

[7] DU YL,LONG ZB,HAN B. Advance in research of thrombosis in paroxysmal nocturnal hemoglobinuria[J]. Basic Clin Med,2017,37(1):128-132.(in Chinese)杜亚丽，龙章彪，韩冰．阵发性睡眠性血红蛋白尿症与血栓发生的研究进展[J]．基础医学与临床，2017,37(1):128-132.

[8] DOUTRELON C,SKOPINSKI S,BOULON C,et al. Paroxysmal nocturnal hemoglobinuria:An unknown cause of thrombosis?[J]. J Mal Vasc,2015,40(6):384-390.

[9] DEZERN AE,BRODSKY RA. Paroxysmal nocturnal hemoglobinuria:A complement-mediated hemolytic anemia[J]. Hematol Oncol Clin North Am,2015,29(3):479-494.

[10] HOEKSTRA J,LEEBEEK FW,PLESSIER A,et al. Paroxysmal nocturnal hemoglobinuria in Budd-Chiari syndrome:Findings from a cohort study[J]. J Hepatol,2009,51(4):696-706.

[11] QI X,HE C,HAN G,et al. Prevalence of paroxysmal nocturnal hemoglobinuria in Chinese patients with Budd-Chiari syndrome or portal vein thrombosis[J]. J Gastroenterol Hepatol,2013,28(1):148-152.

施引文献

资源附件(0)

访问统计