原发性硬化性胆管炎伴IgG4升高1例报告

陈庆灵; 仲瑞; 方伊娜; 张晓雪; 冯丽娜; 杨倩倩; 温晓玉; 金清龙

doi:10.3969/j.issn.1001-5256.2019.09.035

原发性硬化性胆管炎伴IgG4升高1例报告

DOI: 10.3969/j.issn.1001-5256.2019.09.035

1. 吉林大学第一医院肝胆胰内科
2. 吉林大学第一医院神经内科

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中图分类号: R575.7
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出版历程
- 出版日期: 2019-09-20

Primary sclerosing cholangitis with elevated IgG4 levels: A case report

Department of Hepatology, The First Hospital of Jilin University

摘要

摘要: <正>原发性硬化性胆管炎（PSC）是一种慢性进展性胆汁淤积性肝病,其典型的病理改变为胆管炎症及胆管周围同心圆性洋葱皮样纤维化、肝内外胆管破坏导致多灶性胆管狭窄,最终可发展为肝硬化、肝衰竭甚至死亡,此病虽然少见,但其发病率逐年上升[1]。IgG 4相关性硬化性胆管炎（IgG 4-related sclerosing cholangitis,IgG 4-SC）的概念是由Bjornsson等[2]于2007年首先提出,是指一类以胆管周围IgG 4阳性浆细胞浸润及纤维化
- 胆管炎,硬化性 /
- 免疫球蛋白G /
- 诊断 /
- 肝移植
- cholangitis, sclerosing /
- immunoglobulin G /
- diagnosis /
- liver transplantation

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参考文献(22)

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