自身抗体阴性的自身免疫性肝炎重叠原发性胆汁性胆管炎及原发性硬化性胆管炎1例报告

孟淼; 胡臻; 龚镭; 陆忠华; 彭晓斌; 唐学军; 王小云

doi:10.3969/j.issn.1001-5256.2019.08.032

自身抗体阴性的自身免疫性肝炎重叠原发性胆汁性胆管炎及原发性硬化性胆管炎1例报告

DOI: 10.3969/j.issn.1001-5256.2019.08.032

无锡市第二人民医院消化内科

基金项目:

江苏省青年重点人才项目(QNRC2016151)；江苏省自然面上项目(BK20151116)；

详细信息

中图分类号: R575
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出版历程
- 出版日期: 2019-08-20

Autoantibody-negative autoimmune hepatitis overlapping with primary biliary cholangitis and primary sclerosing cholangitis: A case report

Department of Gastroenterology, The Second People's Hospital of Wuxi

Research funding:

摘要

摘要: <正>自身免疫性肝病是一组病因不明、免疫介导的肝损伤,包括自身免疫性肝炎（AIH）、原发性胆汁性胆管炎（PBC）、原发性硬化性胆管炎（PSC）[1],其患病率分别为25/10万～40/10万、17/10万及0. 9/10万～1. 3/10万[2-4]。临床上有小部分患者同时或在病程的不同阶段,具有其中两种或两种以上疾病的临床、生化、免疫及组织学特征时称为重叠综合征[5],报道较多的主要有AIH/PBC、AIH/PSC两种类型。AIH/PBC重叠综合征存在于8%～10%的AIH或PBC患者中[6-7],AIH/PSC重叠综
- 肝炎,自身免疫性 /
- 原发性胆汁性胆管炎 /
- 胆管炎,硬化性
- hepatitis, autoimmune /
- primary biliary cholangitis /
- cholangitis, sclerosing

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参考文献(22)

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