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VHL综合征伴胰腺多发囊肿和第4脑室血管母细胞瘤1例报告

庄春雨 陈小菁 陈家诚 周开伦

引用本文:
Citation:

VHL综合征伴胰腺多发囊肿和第4脑室血管母细胞瘤1例报告

DOI: 10.3969/j.issn.1001-5256.2019.04.034
基金项目: 

国家自然科学基金资助项目(81660489); 

详细信息
  • 中图分类号: R596;R739.4

VHL syndrome with multiple pancreatic cysts and fourth ventricle hemangioblastoma: A case report

Research funding: 

 

  • 摘要:

    <正>范希佩尔-林道(von Hippel Lindau,VHL)综合征是一组临床上较为罕见的多发性、家族性、累及多系统、多脏器的良恶性肿瘤综合征。可累及到的主要器官有脑、脊髓、视网膜、肾脏、肾上腺、胰腺或者附睾等[1]。德国眼科医生von Hippel在1904年第一个描述了眼球内血管瘤的病例,以及Lindau在1927年描述了小脑及脊髓内血管瘤的病例,后人以两位科学家的名字命名此病[2]。本文总结1例VHL综合征患者资料,希

     

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