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无症状Caroli病1例报告

曹丹 辛杰晶 陈延平

引用本文:
Citation:

无症状Caroli病1例报告

DOI: 10.3969/j.issn.1001-5256.2018.06.034
基金项目: 

陕西省重点研发计划项目(2017SF-269); 延安市科技创新团队建设项目(2017C×TD-02); 

详细信息
  • 中图分类号: R575.7

An asymptomatic case of Caroli disease

Research funding: 

 

  • 摘要: <正>1临床资料患者男性,45岁,因肝功能异常10 d,于2017年8月4日入本院。入院前10 d体检发现肝功能异常(ALT 87 U/L、AST50 U/L),上腹部B超提示肝囊肿,肝光点粗大、不均。自觉无不适,既往体健,否认长期服用药物及大量饮酒史。入院查体:未见明显异常。初步诊断:(1)肝损伤原因待查;(2)肝囊肿。入院化验及检查:肝功能ALT 59 U/L,余各项指标均在正常范围内;免疫球蛋白,铜蓝蛋白,血清铁,转铁蛋白均未见明显异

     

  • [1]JARRY J, LEBLANC F, SARIC J.Monolobar Caroli disease[J].Presse Médicale, 2010, 39 (7-8) :847-848.
    [2]PARADA L, HALLEN MI, TRANBERG K, et al.Clonal chromosomal abnormalities in congenital bile duct dilatation (Caroli's disease) [J].Gut, 1999, 45 (5) :780-782.
    [3]OBUSEZ EC, UDAYASANKAR U.Autosomal recessive polycystic kidney disease with Caroli syndrome[J].J Urol, 2015, 193 (2) :679-680.
    [4]GUNAY-AYGUN M.Liver and kidney disease in ciliopathies[J].Am J Med Genet C Semin Med Genet, 2009, 151C (4) :296-306.
    [5]WU KL, CHANGCHIEN CS, KUO CM, et al.Caroli's disease—a report of two siblings[J].Eur J Gastroenterol Hepatol, 2002, 14 (12) :1397-1399.
    [6]PERRICONE G, VANZULLI A.Hepatology:"Central dot sign"of Caroli syndrome[J].J Gastroenterol Hepatol, 2015, 30 (2) :234.
    [7]TODANI T, WATANABE Y, TOKI A, et al.Classification of congenital biliary cystic disease:Special reference to type Ic and IVA cysts with primary ductal stricture[J].J Hepatobiliary Pancreat Surg, 2003, 10 (5) :340-344.
    [8]DONG JH, ZHENG XH, XIA HT, et al.Cysticdilation of bileduct:New clinical classification and treatment strategy[J].Chin J Dig Surg, 2013, 12 (5) :370-377. (in Chinese) 董家鸿, 郑秀海, 夏红天, 等.胆管囊状扩张症:新的临床分型与治疗策略[J].中华消化外科杂志, 2013, 12 (5) :370-377.
    [9]YANG SZ, XIANG CH.Surgical treatment of congenital bile duct dilatation with involvement of the intrahepatic bile duct:Advances, difficulties, and controversy[J].J Clin Hepatol, 2017, 33 (2) :263-267. (in Chinese) 杨世忠, 项灿宏.累及肝内胆管的先天性胆管扩张症:外科治疗的进展、难点与争议[J].临床肝胆病杂志, 2017, 33 (2) :263-267.
    [10] Section of Biliary Surgery, Branch of Surgery, Chinese Medical Association.Guideline for the diagnosis and treatment for biliary dilatation (2017 edition) [J].Chin J Dig Surg, 2017, 16 (8) :767-774. (in Chinese) 中华医学会外科学分会胆道外科学组.胆管扩张症诊断与治疗指南 (2017版) [J].中华消化外科杂志, 2017, 16 (8) :767-774.
    [11]de KERCKHOVE L, de MEYER M, VERBAANDERT C, et al.The place of liver transplantation in Caroli's disease and syndrome[J].Transpl Int, 2006, 19 (5) :381-388.
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  • 出版日期:  2018-06-20
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