中文English
ISSN 1001-5256 (Print)
ISSN 2097-3497 (Online)
CN 22-1108/R

留言板

尊敬的读者、作者、审稿人, 关于本刊的投稿、审稿、编辑和出版的任何问题, 您可以本页添加留言。我们将尽快给您答复。谢谢您的支持!

姓名
邮箱
手机号码
标题
留言内容
验证码

原发性胆汁性肝硬化/原发性硬化性胆管炎重叠综合征合并狼疮性脂膜炎1例报告

魏华芳 周长玉

引用本文:
Citation:

原发性胆汁性肝硬化/原发性硬化性胆管炎重叠综合征合并狼疮性脂膜炎1例报告

DOI: 10.3969/j.issn.1001-5256.2016.06.032
详细信息
  • 中图分类号: R593.24;R575

  • 摘要: <正>1病例资料患者女性,51岁,因"发现肝功能异常7年,乏力1年"于2015年8月11日入院。患者主要不适为乏力,无皮肤瘙痒、高脂血症及脂肪瘤等表现。既往1994年因"口腔溃疡、面部及双上肢散在皮下结节"于吉林大学第一医院诊断为"红斑狼疮",并予皮质醇激素治疗(具体剂量及时间不详),症状缓解。

     

  • [1]YOU H,SUN YM,JIA JD.Progress in autommune liver diseases[J].Chin J Hepatol,2013,21(2):87-89.(in Chinese)尤红,孙亚朦,贾继东.自身免疫性肝病的研究进展[J].中华肝脏病杂志,2013,21(2):87-89.
    [2]LIU C,XU CY,LI GD,et al.Analysis of clinical features of patients with autoimmune hepatitis/primary biliary cirrhosis overlap syndrome[J].J Jilin Univ:Med Edit,2014,40(3):646-649.(in Chinese)刘晨,徐长妍,李国东,等.自身免疫性肝炎/原发性胆汁性肝硬化重叠综合征患者临床特征分析[J].吉林大学学报:医学版,2014,40(3):646-649.
    [3]CZAJA AJ.Frequency and nature of the variant syndromes of autoimmune liver disease[J].Hepatology,1998,28(2):360-365.
    [4]CHAZOUILLERES O,WENDUM D,SERFATY L,et al.Primary biliary cirrhosis-autoimmune hepatitis overlap syndrome:clinical features and response to therapy[J].Hepatology,1998,28(2):296-301.
    [5]MURATORI L,CASSANI F,PAPPAS G,et al.The hepatitic/cholestatic“overlap”syndrome:an Italian experience[J].Autoimmunity,2002,35(8):565-568.
    [6]BOBERG KM,FAUSA O,HAALAND T,et al.Features of autoimmune hepatitis in primary sclerosing cholangitis:an evaluation of 114primary sclerosing cholangitis patients according to a scoring system for the diagnosis of autoimmune hepatitis[J].Hepatology,1996,23(6):1369-1376.
    [7]GREGORIO GV,PORTMANN B,KARANI J,et al.Autoimmune hepatitis/sclerosing cholangitis overlap syndrome in childhood:a 16-year prospective study[J].Hepatology,2001,33(3):544-553.
    [8]FLOREANI A,MOTTA R,CAZZAGON N,et al.The overlap syndrome between primary biliary cirrhosis and primary sclerosing cholangitis[J].Dig Liver Dis,2015,47(5):432-435.
    [9]LINDOR KD,GERSHWIN ME,POUPON R,et al.Primary biliary cirrhosis[J].Hepatology,2009,50(1):291-308.
    [10]HOV JR,BOBERG KM,KARLSEN TH.Autoantibodies in primary sclerosing cholangitis[J].World J Gastroenterol,2008,14(24):3781-3791.
    [11]INVERNIZZI P,LLEO A,PODDA M.Interpreting serological tests in diagnosing autoimmune liver diseases[J].Semin Liver Dis,2007,27(2):161-172.
    [12]KAPLAN MM,GERSHWIN ME.Primary biliary cirrhosis[J].NEngl J Med,2005,353(12):1261-1273.
    [13]WANG T,LI X,LIU YH,et al.Lupus erythematosus panniculitis:clinical and histopathological analysis of 22 cases[J].Acta Acad Med Sin,2011,33(5):525-528.(in Chinese)王涛,李鑫,刘跃华,等.22例狼疮性脂膜炎临床和病理分析[J].中国医学科学院学报,2011,33(5):525-528.
    [14]ESPRITO SANTO J,GOMES MF,GOMES MJ,et al.Intravenous immunoglobulinin lupus panniculitis[J].Clin Rev Allergy Immunol,2010,38(2-3):307-318.
  • 加载中
计量
  • 文章访问数:  1968
  • HTML全文浏览量:  12
  • PDF下载量:  419
  • 被引次数: 0
出版历程
  • 出版日期:  2016-06-20
  • 分享
  • 用微信扫码二维码

    分享至好友和朋友圈

目录

    /

    返回文章
    返回