多囊肝病的研究进展

田辉

多囊肝病的研究进展

田辉

沈阳医学院第三临床学院感染科

详细信息

中图分类号: R575
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出版历程
- 出版日期: 2011-04-20

Advances on the polycystic liver diseases

Tian Hui

摘要

摘要: 多囊肝病(PCLD)是种遗传病,病因复杂,表型表现多样。按遗传方式其又分为常染色体显性遗传PCLD和常染色体隐性遗传PCLD。PCLD囊肿上皮初级纤毛异常及其对多种生长因子增殖效应的敏感性,为将来治疗提供了靶位。
- 肝疾病 /
- 囊肿
Abstract: Polycystic liver diseases (PCLDs) are genetic disorders with heterogeneous etiologies and a range of phenotypic presentations.PCLD exhibits both autosomal or recessive dominant pattern of inheritance.The abnormalities of primary cilia and the sensitivity to proliferative effects of different growth factors in PCLD cystic epithelium provide the basis for future treatment targets.
- liver diseases /
- cysts

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参考文献(21)

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