氨溴索治疗戈谢病相关肝硬化门静脉高压症1例报告

基金项目:

国家自然科学基金面上项目 (81270544)

利益冲突声明：所有作者均声明不存在利益冲突。

作者贡献声明：张玮负责资料分析，撰写论文；崔仕元、王珊珊、郑美芳、张鹏参与收集数据，修改论文；高润平负责拟定写作思路，指导撰写文章并最后定稿。

详细信息

Ambroxol for treatment of liver cirrhosis and portal hypertension in Gaucher disease: A case report

Department of Hepatology, The First Hospital of Jilin University, Changchun 130021, China

图 1 肝脏CT结果

注：a，肝体积增大，门静脉主干明显增宽(白色箭头)；b，氨溴索治疗6个月门静脉主干无明显增宽(白色箭头)。

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图 2 胃镜结果

注：食道下端重度静脉曲张。

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图 3 肝活检病理结果

注：a，肝腺泡结构紊乱，汇管区纤维化和桥接纤维化，假小叶形成(HE染色，×100)；b，肝窦及汇管区可见大量胞浆淡染和皱褶的戈谢细胞(白色箭头) (HE染色，×400)。

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